Outcomes Of Cochlear Implantation In Severe Inner Ear Malformation

Objective To evaluate clinical outcomes of patients with severe inner ear malformation,who received cochlear implantation in Xi Jing Hospital;Methods:21 patients(8 boys and 13 girls)with severe inner ear malformation underwent cochlear implantation from Jan 2018 to June 2019.the mean age at implantation is 3.31 y.Among them,2 patients have Common Cavity,2 patients are Incomplete partition type I(IP-I),4 are Incomplete partition type II(IP-2)and 2 are Incomplete partition type III(IP-III).The most common type is cochlear hypoplasia(11),10 of which have cochlear nerve hypoplasia or aplasia.Their medical records were collected including demography information,preoperation auditory details,and surgical complications.Follow up was made from 6 to 24 month.In the mean time,children with normal inner ear anatomy who underwent cochlear implantation are enrolled in as control group.categories of auditory performance(CAP)、speech intelligibility rating(SIR)、infant-toddler meaningful auditory integration scale(IT-MAIS)、meaningful use of speech scale(MUSS)are exploited as criteria of auditory and speech progress.Results: The CAP and SIR scores gradually increased during the first year after implantation,and there are no obvious deviation between malformation group and normal anatomy group in the first year(p>0.05).However,the IT-MAIS scores in inner ear malformation group may not be as well as that in normal group in the first half year(p<0.05).cochlear nerve deficiency group shows less progress than control group in the first year after cochlear implantationConclusion: cochlear implantation yield relatively good results for sensorineural deafness patients with inner ear malformation,comparing with normal anatomy patients,but larger samples and further follow-up will be made for satisfying results.the benefit of CI in cochlear nerve deficiency children prove limited...